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ASL/Argininosuccinate Lyase Antibody

ASL/Argininosuccinate Lyase Antibody size: 0.1ml 263

Supplier BIOSS PRIMARY UNCONJUGATED ANTIBODIES
Price 263
Size 0.1ml
Contact us Ask Component cell markers and DNA bp. markers are genetic markerser genes or DNA sequenceswith selection audit
Long nameASL/Argininosuccinate Lyase Antibody
Also known asASL/Argininosuccinate Lyase Antibody
CategoryPrimary Antibodies
ConjugationUnconjugated
Target AntigenASL/Argininosuccinate Lyase
SpecificityThis is a highly specific antibody against ASL/Argininosuccinate Lyase
Modification(s)None
Modification site(s)Unmodified antibody
ClonalityPolyclonal antibody
Clone numberPolyclonal antibody
Concentration1ug per 1ul
SourceThis antibody was obtained by immunization of the host with KLH conjugated synthetic peptide derived from human ASL/Argininosuccinate Lyase
Gene ID number435
Tested Applications IF(IHC-P), IHC-P, WB
Recommended dilutions IF(IHC-P)(1:50-200), IHC-P(1:100-500), WB(1:100-1000)
Cross reactivity Mouse, Rat, Human
Cross reactive species details not every possible cross-reactivity is known, Due to limited amount of testing and knowledge
Background of the target antigen ASL catalyzes the hydrolytic cleavage of argininosuccinic acid (ASA) to fumarate and arginine, ASL shares high sequence homology with the avian and reptilian eye lens protein, In addition, Localizing to the cytoplasm and existing as a homotetramer, Mutations in the gene encoding ASL leads to an accumulation of ASA in body fluids and results in Arginosuc-cinic aciduria (ASAuria), This reaction is also involved in the biosynthesis of arginine, an autosomal recessive disorder that is characterized by hyperammonemia, an essential step of the urea cycle which is crucial for the detoxification of ammonia, convulsions, d-crystallin, episodic unconsciousness and dry and brittle hair showing trich-orrhexis nodosa (weak points or nodes in the hair shaft), liver enlargement, physical and mental retardation, ASL is a member of the lyase 1 family of proteins and is predominantly expressed in the liver
Purification methodThis antibody was purified via Protein A
Storage conditions 50% glycerol and 0, Store at -20°, 09% sodium azide, C for up to 1 year, Keep the antibody in aqueous buffered solution containing 1% BSA
Synonym names ARLY_HUMAN, ASAL, ASL, Argininosuccinate lyase, Arginosuccinase, EC 4, 1, 2, 3, Argininosuccinase
PropertiesC, C for long term storage and for short term at + 5°, If you buy Antibodies supplied by Bioss Primary Unconjugated Antibodies they should be stored frozen at - 24°
Gene targetASL/Argininosuccinate Lyase
Short nameASL/Argininosuccinate Lyase Antibody
Technique antibodies against human proteins, antibodies for, Antibody
Alternative nameASL/Argininosuccinate Lyase (Antibody to)
Alternative techniqueantibodies
Identity 746
Gene ASL
Long gene name argininosuccinate lyase
Locus 7q11, 21
Discovery year 2001-06-22
Entrez gene record 435
RefSeq identity NM_000048
Havana BLAST/BLAT OTTHUMG00000022876
Locus Specific Databases LOVD - Leiden Open Variation Database

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