Name : ASL/Argininosuccinate Lyase Antibody, ALEXA FLUOR 594
Supplier : BIOSS PRIMARY CONJUGATED ANTIBODIES
Price :332
SKU : GEN7385442403
| Long name | ALEXA FLUOR 594 Conjugated, ASL/Argininosuccinate Lyase Antibody |
| Also known as | Anti-ASL/Argininosuccinate Lyase PAb ALEXA FLUOR 594 |
| Category | Conjugated Primary Antibodies |
| Conjugated with | 594, ALEXA FLUOR® |
| Host Organism | Rabbit (Oryctolagus cuniculus) |
| Target Antigen | ASL/Argininosuccinate Lyase |
| Specificity | This is a highly specific antibody against ASL/Argininosuccinate Lyase |
| Modification | Unmodified |
| Modification Site | None |
| Clonality | Polyclonal |
| Clone | Polyclonal antibody |
| Concentration | 1ug per 1ul |
| Source | This antibody was obtained by immunization of the host with KLH conjugated synthetic peptide derived from human ASL/Argininosuccinate Lyase |
| Gene ID Number | 435 |
| Tested applications | IF(IHC-P) |
| Recommended dilutions | IF(IHC-P)(1:50-200) |
| Crossreactivity | Mouse, Rat, Human |
| Cross-reactive species details | not every possible cross-reactivity is known, Due to limited amount of testing and knowledge |
| Background of the antigen | ASL catalyzes the hydrolytic cleavage of argininosuccinic acid (ASA) to fumarate and arginine, ASL shares high sequence homology with the avian and reptilian eye lens protein, In addition, Localizing to the cytoplasm and existing as a homotetramer, Mutations in the gene encoding ASL leads to an accumulation of ASA in body fluids and results in Arginosuc-cinic aciduria (ASAuria), This reaction is also involved in the biosynthesis of arginine, an autosomal recessive disorder that is characterized by hyperammonemia, an essential step of the urea cycle which is crucial for the detoxification of ammonia, convulsions, d-crystallin, episodic unconsciousness and dry and brittle hair showing trich-orrhexis nodosa (weak points or nodes in the hair shaft), liver enlargement, physical and mental retardation, ASL is a member of the lyase 1 family of proteins and is predominantly expressed in the liver |
| Purification | Purified by Protein A |
| Storage conditions | 50% glycerol and 0, Keep refrigerated at 2 to 8 degrees Celcius for up to one year, 09% sodium azide, Store this antibody in aqueous buffered solution containing 1% BSA |
| Excitation emission | 590nm/617nm |
| Properties | ALEXA FLUOR they should be stored frozen at - 24°, If you buy Antibodies supplied by Bioss Primary Conjugated Antibodies, C, C for long term storage and for short term at + 5°, For facs or microscopy Alexa 1 conjugate |
| Conjugation | 594, ALEXA FLUOR®, Alexa Fluor |
| Conjugated | Alexa conjugate 1 |
| Gene target | ASL/Argininosuccinate Lyase |
| Short name | ASL/Argininosuccinate Lyase Antibody |
| Technique | antibodies against human proteins, antibodies for, Antibody |
| Label | ALEXA FLUOR 594 |
| Alternative name | ALEXA FLUOR 594, ASL/Argininosuccinate Lyase (Antibody to) |
| Alternative technique | antibodies |
| Identity | 746 |
| Gene | ASL |
| Long gene name | argininosuccinate lyase |
| Locus | 7q11, 21 |
| Discovery year | 2001-06-22 |
| Entrez gene record | 435 |
| RefSeq identity | NM_000048 |
| Havana BLAST/BLAT | OTTHUMG00000022876 |
| Locus Specific Databases | LOVD - Leiden Open Variation Database |