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ATXN3L Antibody, ALEXA FLUOR 594

ATXN3L Antibody, ALEXA FLUOR 594 size: 100ul 332

Price 332
Size 100ul
Long name ALEXA FLUOR 594 Conjugated, ATXN3L Polyclonal Antibody
Also known asAnti-ATXN3L PAb ALEXA FLUOR 594
CategoryConjugated Primary Antibodies
Conjugated with 594, ALEXA FLUOR®
Host OrganismRabbit (Oryctolagus cuniculus)
Target AntigenATXN3L
SpecificityThis is a highly specific antibody against ATXN3L
ModificationUnmodified
Modification SiteNone
ClonalityPolyclonal
ClonePolyclonal antibody
Concentration1ug per 1ul
SourceThis antibody was obtained by immunization of the host with KLH conjugated synthetic peptide derived from human ATXN3L
Gene ID Number92552
Tested applicationsIF(IHC-P)
Recommended dilutionsIF(IHC-P)(1:50-200)
CrossreactivityHuman
Cross-reactive species details not every possible cross-reactivity is known, Due to limited amount of testing and knowledge
Background of the antigen Longer expansions result in earlier onset and more severe clinical manifestations of the disease, Patients show progressive incoordination of gait and often poor coordination of hands, SCA3 belongs to the autosomal dominant cerebellar ataxias type I (ADCA I) which are characterized by cerebellar ataxia in combination with additional clinical features like optic atrophy, Spinocerebellar ataxia is a clinically and genetically heterogeneous group of cerebellar disorders, The molecular defect in SCA3 is the a CAG repeat expansion in ATXN3 coding region, also known as Machado-Joseph disease (MJD), bulbar and extrapyramidal signs, due to degeneration of the cerebellum with variable involvement of the brainstem and spinal cord, ophthalmoplegia, peripheral neuropathy and dementia, speech and eye movements, Defects in ATXN3 are the cause of spinocerebellar ataxia type 3 (SCA3)
PurificationPurified by Protein A
Storage conditions 50% glycerol and 0, Keep refrigerated at 2 to 8 degrees Celcius for up to one year, 09% sodium azide, Store this antibody in aqueous buffered solution containing 1% BSA
Excitation emission590nm/617nm
Synonyms MJDL
Properties ALEXA FLUOR they should be stored frozen at - 24°, If you buy Antibodies supplied by Bioss Primary Conjugated Antibodies, C, C for long term storage and for short term at + 5°, For facs or microscopy Alexa 1 conjugate
Conjugation 594, ALEXA FLUOR®, Alexa Fluor
ConjugatedAlexa conjugate 1
Gene targetATXN3L
Short nameATXN3L Antibody
Technique antibodies against human proteins, antibodies for, Antibody
LabelALEXA FLUOR 594
Alternative name ALEXA FLUOR 594, ATXN3L (Antibody to)
Alternative techniqueantibodies
Identity 24173
Gene ATXN3L
Long gene name ataxin 3 like
Synonyms gene name ataxin 3-like
Locus Xp22, 2
Discovery year 2004-08-20
Entrez gene record 92552
RefSeq identity NM_001135995
Classification MJD deubiquinating enzymes
Havana BLAST/BLAT OTTHUMG00000021146
Locus Specific Databases Mental Retardation database

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