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CABC1 Antibody, FITC Conjugated

CABC1 Antibody, FITC Conjugated size: 0.1ml 333

Supplier BIOSS PRIMARY CONJUGATED ANTIBODIES 1
Price 333
Size 0.1ml
Contact us Ask Component cell markers and DNA bp. markers are genetic markerser genes or DNA sequenceswith selection audit
Long name FITC Conjugated, CABC1 Polyclonal Antibody
CategoryConjugated Primary Antibodies
ConjugationAnti-FITC Antibody
Host OrganismRabbit (Oryctolagus cuniculus)
Target AntigenCABC1
SpecificityThis is a highly specific antibody against CABC1
ModificationUnmodified
Modification siteNone
ClonalityPolyclonal
ClonePolyclonal antibody
Concentration1ug per 1ul
SourceKLH conjugated synthetic peptide derived from human ADCK3/CABC1
Tested applicationsIF(IHC-P)
Recommended dilutionsIF(IHC-P)(1:50-200)
Crossreactivity Mouse, Rat, Human
Crossreactive species details not every possible cross-reactivity is known, Due to limited amount of testing and knowledge
Antigen background CoQ10 deficiency is an autosomal recessive disorder with variable manifestations, It can be associated with three main clinical phenotypes: a predominantly myopathic form with central nervous system involvement, Patients can manifest brisk tendon reflexes and Hoffmann sign, Patients show progressive incoordination of gait and often poor coordination of hands, SCAR9 is an autosomal recessive form characterized by gait ataxia and cerebellar atrophy with slow progression and few associated features, Spinocerebellar ataxia is a clinically and genetically heterogeneous group of cerebellar disorders, also known as autosomal recessive cerebellar ataxia type 2 (ARCA2), an infantile encephalomyopathy with renal dysfunction and an ataxic form with cerebellar atrophy, due to degeneration of the cerebellum with variable involvement of the brainstem and spinal cord, exercise intolerance and elevated serum lactate, mild axonal degeneration of the sural nerve, mild psychomotor retardation, speech and eye movements, Defects in ADCK3 are the cause of spinocerebellar ataxia autosomal recessive type 9 (SCAR9) [MIM:612016], Involvement in disease:Defects in ADCK3 are a cause of coenzyme Q10 deficiency (CoQ10 deficiency), May be a chaperone-like protein essential for the proper conformation and functioning of protein complexes in the respiratory chain, Tissue specificity:Ubiquitously expressed with a relatively greater abundance in heart and skeletal muscle
Purification methodThis antibody was purified via Protein A
Storage conditions 50% glycerol and 0, Store refrigerated at 2 to 8 degrees Celcius for up to 1 year, 09% sodium azide, Keep the antibody in an aqueous buffered solution containing 1% BSA
Excitation Emission494nm/518nm
Synonyms COQ8 SCAR9
Properties Bioss Primary Conjugated Antibodies FITC is highly sensitive to pH extremes, FITC has a green emission that's usually collected at 530 nanometers, FITC has a high quantum yield (efficiency of energy transfer from absorption to emission fluorescence) and approximately half of the absorbed photons are emitted as fluorescent light, For fluorescent microscopy applications, This Bioss Primary Conjugated Antibodies Fluorescein isothiocyanate (FITC) antibody is currently after some BD antibodies the most commonly used fluorescent dye for FACS, When excited at 488 nanometers, its photo bleaching effects are not observed due to a very brief interaction at the laser intercept, the 1 FITC is seldom used as it photo bleaches rather quickly though in flow cytometry applications, the FL1 detector of a FACSCalibur or FACScan, C, C for long term storage and for short term at + 5°, If you buy Antibodies supplied by Bioss Primary Conjugated Antibodies they should be stored frozen at - 24°
Gene targetCABC1 Conjugated
Short name FITC Conjugated, CABC1 Antibody
Technique Fluorescein, antibodies against human proteins, antibodies for, antibody Conjugates, Antibody
LabelFITC
Alternative name fluorecein coupled, CABC1 (Antibody to)
Alternative techniqueantibodies
Identity 16812
Gene COQ8A
Long gene name coenzyme Q8A
Synonyms gene CABC1 ADCK3
Synonyms gene name ABC1 activity of bc1 complex homolog (S, ABC1 activity of bc1 complex like (S, S, chaperone-ABC1 (activity of bc1 complex, pombe) aarF domain containing kinase 3 , pombe) chaperone, pombe)-like chaperone
Synonyms name coenzyme Q8 homolog (yeast)
Locus 1q42, 13
Discovery year 2001-10-31
GenBank acession AJ278126
Entrez gene record 56997
Pubmed identfication 18319072 18319074 25498144
RefSeq identity NM_020247
Havana BLAST/BLAT OTTHUMG00000037621
Locus Specific Databases LRG_1092

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