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Galactosidase alpha Antibody, ALEXA FLUOR 594

Galactosidase alpha Antibody, ALEXA FLUOR 594 size: 100ul 332

Price 332
Size 100ul
Long name ALEXA FLUOR 594 Conjugated, Galactosidase alpha Polyclonal Antibody
Also known asAnti-Galactosidase alpha PAb ALEXA FLUOR 594
CategoryConjugated Primary Antibodies
Conjugated with 594, ALEXA FLUOR®
Host OrganismRabbit (Oryctolagus cuniculus)
Target AntigenGalactosidase alpha
SpecificityThis is a highly specific antibody against Galactosidase alpha
ModificationUnmodified
Modification SiteNone
ClonalityPolyclonal
ClonePolyclonal antibody
Concentration1ug per 1ul
Immunogen range127-148/429
Subcellular locationLysosome
SourceThis antibody was obtained by immunization of the host with KLH conjugated synthetic peptide derived from human Galactosidase alpha
Gene ID Number2717
Swiss ProtP06280
Tested applicationsIF(IHC-P)
Recommended dilutionsIF(IHC-P)(1:50-200)
Crossreactivity Mouse, Rat, Human
Cross-reactive species details not every possible cross-reactivity is known, Due to limited amount of testing and knowledge
Background of the antigen Clinical recognition in males results from characteristic skin lesions (angiokeratomas) over the lower trunk, Death results from renal failure, Defects in GLA are the cause of Fabry's disease (FD), FD is a rare X-linked sphingolipidosis disease where glycolipid accumulates in many tissues, Heterozygous females may exhibit the disorder in an attenuated form, Patients may show ocular deposits, and burning pain in the extremities, cardiac or cerebral complications of hypertension or other vascular disease, febrile episodes, galactomannans and galactohydrolase, including galactose oligosaccharides, non reducing alpha D galactose residues in alpha D galactosides, they are more likely to show corneal opacities, Galactosidase alpha is involved in the hydrolysis of terminal
PurificationPurified by Protein A
Storage conditions 50% glycerol and 0, Keep refrigerated at 2 to 8 degrees Celcius for up to one year, 09% sodium azide, Store this antibody in aqueous buffered solution containing 1% BSA
Excitation emission590nm/617nm
Synonyms GALA
Properties ALEXA FLUOR they should be stored frozen at - 24°, If you buy Antibodies supplied by Bioss Primary Conjugated Antibodies, C, C for long term storage and for short term at + 5°, For facs or microscopy Alexa 1 conjugate
Conjugation 594, ALEXA FLUOR®, Alexa Fluor
ConjugatedAlexa conjugate 1
Gene targetGalactosidase alpha
Short nameGalactosidase alpha Antibody
Technique antibodies against human proteins, antibodies for, Antibody
LabelALEXA FLUOR 594
Alternative name ALEXA FLUOR 594, Galactosidase a (Antibody to)
Alternative techniqueantibodies
Identity 4296
Gene GLA
Long gene name galactosidase alpha
Locus Xq22, 1
Discovery year 2001-06-22
GenBank acession X16889
Entrez gene record 2717
Havana BLAST/BLAT OTTHUMG00000022026
Locus Specific Databases Mental Retardation database LRG_672

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