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GCSH Antibody

GCSH Antibody size: 0.1ml 263

Price 263
Size 0.1ml
Long nameGCSH Primary Polyclonal Antibody
Also known asGCSH PAb
CategoryPrimary Antibodies
ConjugationUnconjugated
Target AntigenGCSH
SpecificityThis is a highly specific antibody against GCSH
Modification(s)None
Modification site(s)Unmodified antibody
ClonalityPolyclonal antibody
Clone numberPolyclonal antibody
Concentration1ug per 1ul
SourceThis antibody was obtained by immunization of the host with KLH conjugated synthetic peptide derived from human GCSH
Gene ID number2653
Tested Applications IF(IHC-P), IHC-P, WB
Recommended dilutions IF(IHC-P)(1:50-200), IHC-P(1:100-500), WB(1:100-1000)
Cross reactivity Mouse, Rat, Human
Cross reactive species details not every possible cross-reactivity is known, Due to limited amount of testing and knowledge
Background of the target antigen Characterized by severe neurological symptoms, Defects in the gene encoding GCSH are the cause of glycine encephalopathy (GCE), The gene encoding GCSH maps to human chromosome 16, an autosomal recessive disease that is also referred to as non-ketotic hyperglycinemia (NKH), patients with GCE have a large amount of glycine accumulated in their body fluids, which encodes over 900 genes and comprises nearly 3% of the human genome, GCSH is a 173 amino acid mitochondrial protein that contains one lipoyl-binding domain and belongs to the gcvH family
Purification methodThis antibody was purified via Protein A
Storage conditions 50% glycerol and 0, Store at -20°, 09% sodium azide, C for up to 1 year, Keep the antibody in aqueous buffered solution containing 1% BSA
Synonym names GCSH, GCSH_HUMAN, Glycine cleavage system H protein, Glycine cleavage system H protein mitochondrial, Glycine cleavage system protein H, Glycine cleavage system protein H aminomethyl carrier, Lipoic acid containing protein, Mitochondrial glycine cleavage system H protein, NKH, mitochondrial, GCE
PropertiesC, C for long term storage and for short term at + 5°, If you buy Antibodies supplied by Bioss Primary Unconjugated Antibodies they should be stored frozen at - 24°
Gene targetGCSH
Short nameGCSH Antibody
Technique antibodies against human proteins, antibodies for, Antibody
Alternative nameGCSH (Antibody to)
Alternative techniqueantibodies
Identity 4208
Gene GCSH
Long gene name glycine cleavage system protein H
Synonyms gene name glycine cleavage system protein H (aminomethyl carrier)
Synonyms name lipoic acid-containing protein
Locus 16q23, 2
Discovery year 1992-04-08
GenBank acession M69175
Entrez gene record 2653
Pubmed identfication 1671321 2025283
RefSeq identity NM_004483
Havana BLAST/BLAT OTTHUMG00000137626
Locus Specific Databases LRG_541

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