Name : GNS/Glucosamine 6 sulfatase Antibody, ALEXA FLUOR 350
Supplier : BIOSS PRIMARY CONJUGATED ANTIBODIES
Price :332
SKU : GEN8188703567
| Long name | ALEXA FLUOR 350 Conjugated, GNS/Glucosamine 6 sulfatase Antibody |
| Also known as | Anti-GNS/Glucosamine 6 sulfatase PAb ALEXA FLUOR 350 |
| Category | Conjugated Primary Antibodies |
| Conjugated with | 350, ALEXA FLUOR® |
| Host Organism | Rabbit (Oryctolagus cuniculus) |
| Target Antigen | GNS/Glucosamine 6 sulfatase |
| Specificity | This is a highly specific antibody against GNS/Glucosamine 6 sulfatase |
| Modification | Unmodified |
| Modification Site | None |
| Clonality | Polyclonal |
| Clone | Polyclonal antibody |
| Concentration | 1ug per 1ul |
| Source | This antibody was obtained by immunization of the host with KLH conjugated synthetic peptide derived from human GNS/Glucosamine 6 sulfatase |
| Gene ID Number | 2799 |
| Tested applications | IF(IHC-P) |
| Recommended dilutions | IF(IHC-P)(1:50-200) |
| Crossreactivity | Mouse, Rat, Human |
| Cross-reactive species details | not every possible cross-reactivity is known, Due to limited amount of testing and knowledge |
| Background of the antigen | A member of the sulfatase family, GNS assists in the catabolism of heparin, GNS deficiency results in an autosomal recessive lysosomal storage disorder known as mucopolysaccharidosis type IIID (Sanfilippo D syndrome), GNS is encoded by a gene mapping to human chromosome 12q14, Subject to post-translational internal peptidase cleavage, and binds calcium as a cofactor, which is characterized by mild somatic disease and severe degeneration of the central nervous system, 2 and mouse chromosome 10 D2, GNS is a 552 amino acid lysosomal enzyme that hydrolyzes the 6-sulfate groups of the N-acetyl-D-glucosamine 6-sulfate units of keratan sulfate and heparan sulfate |
| Purification | Purified by Protein A |
| Storage conditions | 50% glycerol and 0, Keep refrigerated at 2 to 8 degrees Celcius for up to one year, 09% sodium azide, Store this antibody in aqueous buffered solution containing 1% BSA |
| Excitation emission | 343nm/442nm |
| Properties | ALEXA FLUOR they should be stored frozen at - 24°, Alexa Fluor 350 conjugates can be used in multi-color flow cytometry with FACS's equipped with a second red laser or red diode, If you buy Antibodies supplied by Bioss Primary Conjugated Antibodies, C, C for long term storage and for short term at + 5°, For facs or microscopy Alexa 1 conjugate |
| Conjugation | ALEXA FLUOR 350, Alexa Fluor |
| Gene target | GNS/Glucosamine 6 sulfatase |
| Short name | GNS/Glucosamine 6 sulfatase Antibody |
| Technique | antibodies against human proteins, antibodies for, Antibody |
| Label | ALEXA FLUOR 350 |
| Alternative name | ALEXA FLUOR 350, GNS/Glucosamine 6 sulfatase (Antibody to) |
| Alternative technique | antibodies |
| Identity | 4422 |
| Gene | GNS |
| Long gene name | glucosamine (N-acetyl)-6-sulfatase |
| Synonyms name | Sanfilippo disease IIID N-acetylglucosamine-6-sulfatase |
| Locus | 12q14, 3 |
| Discovery year | 1988-06-09 |
| Entrez gene record | 2799 |
| Classification | Sulfatases |
| Havana BLAST/BLAT | OTTHUMG00000168819 |