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HIBADH Antibody

HIBADH Antibody size: 0.1ml 263

Supplier BIOSS PRIMARY UNCONJUGATED ANTIBODIES
Price 263
Size 0.1ml
Contact us Ask Component cell markers and DNA bp. markers are genetic markerser genes or DNA sequenceswith selection audit
Long nameHIBADH Primary Polyclonal Antibody
Also known asHIBADH PAb
CategoryPrimary Antibodies
ConjugationUnconjugated
Target AntigenHIBADH
SpecificityThis is a highly specific antibody against HIBADH
Modification(s)None
Modification site(s)Unmodified antibody
ClonalityPolyclonal antibody
Clone numberPolyclonal antibody
Concentration1ug per 1ul
SourceThis antibody was obtained by immunization of the host with KLH conjugated synthetic peptide derived from human HIBADH
Gene ID number11112
Tested Applications IF(IHC-P), IHC-P, WB
Recommended dilutions IF(IHC-P)(1:50-200), IHC-P(1:100-500), WB(1:100-1000)
Cross reactivityHuman
Cross reactive species details not every possible cross-reactivity is known, Due to limited amount of testing and knowledge
Background of the target antigen However, It was previously hypothesized that defects in the gene encoding HIBADH may be the cause of 3-Hydroxyisobutyric aciduria, The enzyme functions as a homodimer between a pH of 7, a rare disorder that is characterized by a variety of clinical manifestations such as neurodevelopmental problems and dysmorphic features, an intermediate of valine catabolism, it was shown that HIBADH activity was equal in patients with 3-Hydroxyisobutyric aciduria as compared with controls, reversible oxidization of 3-Hydroxyisobutyrate to methylmalonate semialdehyde, with optimal activity between 8, 0 and 10, 8 and 9, HIBADH is a 336 amino acid mitochondrial enzyme that catalyzes the NAD+-dependent
Purification methodThis antibody was purified via Protein A
Storage conditions 50% glycerol and 0, Store at -20°, 09% sodium azide, C for up to 1 year, Keep the antibody in aqueous buffered solution containing 1% BSA
Synonym names 3 hydroxyisobutyrate dehydrogenase, 3 hydroxyisobutyrate dehydrogenase mitochondrial, 3HIDH_HUMAN, EC 1, MGC40361, NS5ATP1, 1, 1, 3 hydroxy 2 methylpropanoate:NAD+ oxidoreductase, 31
PropertiesC, C for long term storage and for short term at + 5°, If you buy Antibodies supplied by Bioss Primary Unconjugated Antibodies they should be stored frozen at - 24°
Gene targetHIBADH
Short nameHIBADH Antibody
Technique antibodies against human proteins, antibodies for, Antibody
Alternative nameHIBADH (Antibody to)
Alternative techniqueantibodies
Identity 4907
Gene HIBADH
Long gene name 3-hydroxyisobutyrate dehydrogenase
Synonyms NS5ATP1
Locus 7p15, 2
Discovery year 1999-08-05
GenBank acession AF529362
Entrez gene record 11112
RefSeq identity NM_152740
Havana BLAST/BLAT OTTHUMG00000097035

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