Name : HIBADH Antibody, Biotin Conjugated
Supplier : BIOSS PRIMARY CONJUGATED ANTIBODIES 1
Price :333
SKU : GEN9829757475
| Long name | Biotin Conjugated, HIBADH Polyclonal Antibody |
| Category | Conjugated Primary Antibodies |
| Conjugation | Biotinylated |
| Host Organism | Rabbit (Oryctolagus cuniculus) |
| Target Antigen | HIBADH |
| Specificity | This is a highly specific antibody against HIBADH |
| Modification | Unmodified |
| Modification site | None |
| Clonality | Polyclonal |
| Clone | Polyclonal antibody |
| Concentration | 1ug per 1ul |
| Source | KLH conjugated synthetic peptide derived from human HIBADH |
| Gene ID number | 11112 |
| Tested applications | IHC-P, WB |
| Recommended dilutions | IHC-P(1:100-500), WB(1:100-1000) |
| Crossreactivity | Human |
| Crossreactive species details | not every possible cross-reactivity is known, Due to limited amount of testing and knowledge |
| Antigen background | However, It was previously hypothesized that defects in the gene encoding HIBADH may be the cause of 3-Hydroxyisobutyric aciduria, The enzyme functions as a homodimer between a pH of 7, a rare disorder that is characterized by a variety of clinical manifestations such as neurodevelopmental problems and dysmorphic features, an intermediate of valine catabolism, it was shown that HIBADH activity was equal in patients with 3-Hydroxyisobutyric aciduria as compared with controls, reversible oxidization of 3-Hydroxyisobutyrate to methylmalonate semialdehyde, with optimal activity between 8, 0 and 10, 8 and 9, HIBADH is a 336 amino acid mitochondrial enzyme that catalyzes the NAD+-dependent |
| Purification method | This antibody was purified via Protein A |
| Storage conditions | 50% glycerol and 0, Store refrigerated at 2 to 8 degrees Celcius for up to 1 year, 09% sodium azide, Keep the antibody in an aqueous buffered solution containing 1% BSA |
| Excitation Emission | N/A |
| Synonyms | NS5ATP1 |
| Properties | Avidin and Streptavidin bind to the small biotin and are couple to HRP or AP for ELISA, Biotin conjugates can be detected by horseradish peroxidase, To break the streptavidin Biotin bond we suggest to use a 6 molar guanidine HCl solution with acidity of pH 1, alkaline phosphatase substrates or anti biotin conjugated antibodies, 6, C, C for long term storage and for short term at + 5°, If you buy Antibodies supplied by Bioss Primary Conjugated Antibodies they should be stored frozen at - 24° |
| Gene target | HIBADH Conjugated |
| Short name | Conjugated, HIBADH Antibody |
| Technique | antibodies against human proteins, antibodies for, antibody Conjugates, Antibody |
| Label | Biotin |
| Alternative name | biotinilated coupled, HIBADH (Antibody to) |
| Alternative technique | antibodies |
| Identity | 4907 |
| Gene | HIBADH |
| Long gene name | 3-hydroxyisobutyrate dehydrogenase |
| Locus | 7p15, 2 |
| Discovery year | 1999-08-05 |
| GenBank acession | AF529362 |
| Entrez gene record | 11112 |
| RefSeq identity | NM_152740 |
| Havana BLAST/BLAT | OTTHUMG00000097035 |