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HMBS Antibody

HMBS Antibody size: 0.1ml 263

Supplier BIOSS PRIMARY UNCONJUGATED ANTIBODIES
Price 263
Size 0.1ml
Contact us Ask Component cell markers and DNA bp. markers are genetic markerser genes or DNA sequenceswith selection audit
Long nameHMBS Primary Polyclonal Antibody
Also known asHMBS PAb
CategoryPrimary Antibodies
ConjugationUnconjugated
Target AntigenHMBS
SpecificityThis is a highly specific antibody against HMBS
Modification(s)None
Modification site(s)Unmodified antibody
ClonalityPolyclonal antibody
Clone numberPolyclonal antibody
Concentration1ug per 1ul
SourceThis antibody was obtained by immunization of the host with KLH conjugated synthetic peptide derived from human HMBS/PBGD
Gene ID number3145
Tested Applications IF(IHC-P), IHC-P, WB
Recommended dilutions IF(IHC-P)(1:50-200), IHC-P(1:100-500), WB(1:100-1000)
Cross reactivity Mouse, Rat, Human
Cross reactive species details not every possible cross-reactivity is known, Due to limited amount of testing and knowledge
Background of the target antigen AIP is characterized by acute attacks of neurological dysfunctions with hypertension, Deficiency of PBGD causes errors in pyrrole metabolism, PBGD belongs to the HMBS (hydroxymethylbilane synthase) family, abdominal pain and excessive amounts of aminolevulinic acid and porphobilinogen in the urine, also designated hydroxymethylbilane synthase, is a cytoplasmic enzyme found in the heme synthesis pathway, peripheral neurologic disturbances, tachycardia, which in turn leads to an inherited autosomal disorder called acute intermittent porphyria (AIP), PBGD
Purification methodThis antibody was purified via Protein A
Storage conditions 50% glycerol and 0, Store at -20°, 09% sodium azide, C for up to 1 year, Keep the antibody in aqueous buffered solution containing 1% BSA
Synonym names HMBS, Hydroxymethylbilane synthase, PBG D, PBG-D, PBGD, Porphobilinogen deaminase, Pre uroporphyrinogen synthase, Pre-uroporphyrinogen synthase, UPS, Uroporphyrinogen I synthase, Uroporphyrinogen I synthetase, HEM3_HUMAN
PropertiesC, C for long term storage and for short term at + 5°, If you buy Antibodies supplied by Bioss Primary Unconjugated Antibodies they should be stored frozen at - 24°
Gene targetHMBS
Short nameHMBS Antibody
Technique antibodies against human proteins, antibodies for, Antibody
Alternative nameHMBS (Antibody to)
Alternative techniqueantibodies
Identity 4982
Gene HMBS
Long gene name hydroxymethylbilane synthase
Synonyms gene PBGD UPS PORC
Synonyms gene name Chester type , acute, uroporphyrinogen I synthase porphobilinogen deaminase porphyria
Locus 11q23, 3
Discovery year 1986-01-01
GenBank acession X04808
Entrez gene record 3145
Pubmed identfication 8432552 17298217
RefSeq identity NM_000190
Havana BLAST/BLAT OTTHUMG00000168295
Locus Specific Databases LRG_1076

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