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Galactosidase alpha Antibody

Galactosidase alpha Antibody size: 0.1ml 263

Supplier BIOSS PRIMARY UNCONJUGATED ANTIBODIES
Price 263
Size 0.1ml
Contact us Ask Component cell markers and DNA bp. markers are genetic markerser genes or DNA sequenceswith selection audit
Long nameGalactosidase alpha Primary Polyclonal Antibody
Also known asGalactosidase alpha PAb
CategoryPrimary Antibodies
ConjugationUnconjugated
Target AntigenGalactosidase alpha
SpecificityThis is a highly specific antibody against Galactosidase alpha
Modification(s)None
Modification site(s)Unmodified antibody
ClonalityPolyclonal antibody
Clone numberPolyclonal antibody
Concentration1ug per 1ul
Immunogen range127-148/429
Subcellular locationLysosome
SourceThis antibody was obtained by immunization of the host with KLH conjugated synthetic peptide derived from human Galactosidase alpha
Gene ID number2717
Swiss ProtP06280
Tested Applications IF(IHC-P), IHC-P, WB
Recommended dilutions IF(IHC-P)(1:50-200), IHC-P(1:100-500), WB(1:100-1000)
Cross reactivity Mouse, Rat, Human
Cross reactive species details not every possible cross-reactivity is known, Due to limited amount of testing and knowledge
Background of the target antigen Clinical recognition in males results from characteristic skin lesions (angiokeratomas) over the lower trunk, Death results from renal failure, Defects in GLA are the cause of Fabry's disease (FD), FD is a rare X-linked sphingolipidosis disease where glycolipid accumulates in many tissues, Heterozygous females may exhibit the disorder in an attenuated form, Patients may show ocular deposits, and burning pain in the extremities, cardiac or cerebral complications of hypertension or other vascular disease, febrile episodes, galactomannans and galactohydrolase, including galactose oligosaccharides, non reducing alpha D galactose residues in alpha D galactosides, they are more likely to show corneal opacities, Galactosidase alpha is involved in the hydrolysis of terminal
Purification methodThis antibody was purified via Protein A
Storage conditions 50% glycerol and 0, Store at -20°, 09% sodium azide, C for up to 1 year, Keep the antibody in aqueous buffered solution containing 1% BSA
Synonym names Alpha-D-galactosidase A, Alpha-D-galactoside galactohydrolase, Alpha-galactosidase A, GLA, Melibiase, GALA
PropertiesC, C for long term storage and for short term at + 5°, If you buy Antibodies supplied by Bioss Primary Unconjugated Antibodies they should be stored frozen at - 24°
Gene targetGalactosidase alpha
Short nameGalactosidase alpha Antibody
Technique antibodies against human proteins, antibodies for, Antibody
Alternative nameGalactosidase a (Antibody to)
Alternative techniqueantibodies
Identity 4296
Gene GLA
Long gene name galactosidase alpha
Synonyms GALA
Locus Xq22, 1
Discovery year 2001-06-22
GenBank acession X16889
Entrez gene record 2717
Havana BLAST/BLAT OTTHUMG00000022026
Locus Specific Databases Mental Retardation database LRG_672

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