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ATXN3L Antibody

ATXN3L Antibody size: 0.1ml 263

Supplier BIOSS PRIMARY UNCONJUGATED ANTIBODIES
Price 263
Size 0.1ml
Contact us Ask Component cell markers and DNA bp. markers are genetic markerser genes or DNA sequenceswith selection audit
Long nameATXN3L Primary Polyclonal Antibody
Also known asATXN3L PAb
CategoryPrimary Antibodies
ConjugationUnconjugated
Target AntigenATXN3L
SpecificityThis is a highly specific antibody against ATXN3L
Modification(s)None
Modification site(s)Unmodified antibody
ClonalityPolyclonal antibody
Clone numberPolyclonal antibody
Concentration1ug per 1ul
SourceThis antibody was obtained by immunization of the host with KLH conjugated synthetic peptide derived from human ATXN3L
Gene ID number92552
Tested Applications IF(IHC-P), IHC-P, WB
Recommended dilutions IF(IHC-P)(1:50-200), IHC-P(1:100-500), WB(1:100-1000)
Cross reactivityHuman
Cross reactive species details not every possible cross-reactivity is known, Due to limited amount of testing and knowledge
Background of the target antigen Longer expansions result in earlier onset and more severe clinical manifestations of the disease, Patients show progressive incoordination of gait and often poor coordination of hands, SCA3 belongs to the autosomal dominant cerebellar ataxias type I (ADCA I) which are characterized by cerebellar ataxia in combination with additional clinical features like optic atrophy, Spinocerebellar ataxia is a clinically and genetically heterogeneous group of cerebellar disorders, The molecular defect in SCA3 is the a CAG repeat expansion in ATXN3 coding region, also known as Machado-Joseph disease (MJD), bulbar and extrapyramidal signs, due to degeneration of the cerebellum with variable involvement of the brainstem and spinal cord, ophthalmoplegia, peripheral neuropathy and dementia, speech and eye movements, Defects in ATXN3 are the cause of spinocerebellar ataxia type 3 (SCA3)
Purification methodThis antibody was purified via Protein A
Storage conditions 50% glycerol and 0, Store at -20°, 09% sodium azide, C for up to 1 year, Keep the antibody in aqueous buffered solution containing 1% BSA
Synonym names ATXN3L, MJDL, Machado-Joseph disease protein 1-like, Putative ataxin-3-like protein, ATX3L_HUMAN
PropertiesC, C for long term storage and for short term at + 5°, If you buy Antibodies supplied by Bioss Primary Unconjugated Antibodies they should be stored frozen at - 24°
Gene targetATXN3L
Short nameATXN3L Antibody
Technique antibodies against human proteins, antibodies for, Antibody
Alternative nameATXN3L (Antibody to)
Alternative techniqueantibodies
Identity 24173
Gene ATXN3L
Long gene name ataxin 3 like
Synonyms gene name ataxin 3-like
Synonyms MJDL
Locus Xp22, 2
Discovery year 2004-08-20
Entrez gene record 92552
RefSeq identity NM_001135995
Classification MJD deubiquinating enzymes
Havana BLAST/BLAT OTTHUMG00000021146
Locus Specific Databases Mental Retardation database

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